- Featured Product
- KD/KO Validated
BCS1L Monoclonal antibody, PBS Only
BCS1L Monoclonal Antibody for WB, IF, IHC, Indirect ELISA
Host / Isotype
Mouse / IgG1
Reactivity
human, mouse
Applications
WB, IF, IHC, Indirect ELISA
Conjugate
Unconjugated
CloneNo.
3G6H1
Cat no : 60212-1-PBS
Synonyms
Validation Data Gallery
Tested Applications
Recommended dilution
Application | Dilution |
---|---|
It is recommended that this reagent should be titrated in each testing system to obtain optimal results. |
Product Information
60212-1-PBS targets BCS1L in WB, IF, IHC, Indirect ELISA applications and shows reactivity with human, mouse samples.
Tested Reactivity | human, mouse |
Host / Isotype | Mouse / IgG1 |
Class | Monoclonal |
Type | Antibody |
Immunogen | BCS1L fusion protein Ag18280 相同性解析による交差性が予測される生物種 |
Full Name | BCS1-like (yeast) |
Calculated molecular weight | 48 kDa |
Observed molecular weight | 47 kDa |
GenBank accession number | BC007500 |
Gene symbol | BCS1L |
Gene ID (NCBI) | 617 |
Conjugate | Unconjugated |
Form | Liquid |
Purification Method | Protein G purification |
Storage Buffer | PBS Only |
Storage Conditions | Store at -80°C. |
Background Information
Human BCS1-like (BCS1L), a mitochondrial inner-membrane protein, is a chaperone necessary for the assembly of mitochondrial respiratory chain complex III. Recently studies indicated that the mutations in this protein may cause the GRACILE (growth retardation, aminoaciduria, cholestasis, iron overload, lactacidosis, and early death) syndrome, a recessively inherited lethal disease characterized by fetal growth retardation, lactic acidosis, aminoaciduria, cholestasis, and abnormalities in iron metabolism.